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</topic><topic id="https://vocabulario.abcd.usp.br/pt-br/?tema=5158"><instanceOf><topicRef xlink:href="#term"/></instanceOf><baseName><baseNameString>ANENCEFALIA</baseNameString></baseName>  <occurrence>    <instanceOf>      <topicRef xlink:href="#scope-note"/>    </instanceOf><baseName><baseNameString><![CDATA[ Malformação do sistema nervoso causada por falha de fechamento do neuroporo anterior. Os neonatos nascem com medula espinhal, cerebelo e tronco cerebral intactos, porém sem a formação de estruturas neurais acima deste nível. O cérebro é somente parcialmente formado, mas os olhos freqüentemente são normais. Esta afecção pode estar associada com deficiência de folatos. Os neonatos afetados são capazes apenas de reflexos primitivos (tronco encefálico) e normalmente não sobrevivem por mais do que duas semanas. (Tradução livre do original: Menkes, Textbook of Child Neurology, 5th ed, p247).<p>Fonte: DeCS server. Disponível em: http://decs.bvs.br.<p> ]]></baseNameString></baseName>  </occurrence></topic>  <association>    <instanceOf>      <topicRef xlink:href="#broader-narrower"/>    </instanceOf>    <member>      <roleSpec>  <topicRef xlink:href="#narrower"/>      </roleSpec>      <topicRef xlink:href="#https://vocabulario.abcd.usp.br/pt-br/?tema=5158"/>    </member>    <member>      <roleSpec>  <topicRef xlink:href="#broader"/>      </roleSpec>      <topicRef xlink:href="#https://vocabulario.abcd.usp.br/pt-br/?tema=27346"/>    </member>  </association></topicMap>