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</topic><topic id="https://vocabulario.abcd.usp.br/pt-br/?tema=67788"><instanceOf><topicRef xlink:href="#term"/></instanceOf><baseName><baseNameString>NEOPLASIA ENDÓCRINA MÚLTIPLA</baseNameString></baseName>  <occurrence>    <instanceOf>      <topicRef xlink:href="#scope-note"/>    </instanceOf><baseName><baseNameString><![CDATA[ Grupo de doenças autossômicas, dominantes, caracterizado pela ocorrência combinada de tumores envolvendo duas ou mais Glândulas Endócrinas que secretam Hormônios Peptídicos ou Aminas. Estas neoplasias, freqüentemente são benignas, porém podem ser malígnas. São classificadas de acordo com as glândulas endócrinas envolvidas e grau de agressividade. As duas formas principais são MEN1 e MEN2 com mutações gênicas no Cromossono 11 e Cromossomo 10, respectivamente. <p>Fonte: DeCS server. Disponível em: http://decs.bvs.br.<p> ]]></baseNameString></baseName>  </occurrence></topic>  <association>    <instanceOf>      <topicRef xlink:href="#broader-narrower"/>    </instanceOf>    <member>      <roleSpec>  <topicRef xlink:href="#narrower"/>      </roleSpec>      <topicRef xlink:href="#https://vocabulario.abcd.usp.br/pt-br/?tema=67788"/>    </member>    <member>      <roleSpec>  <topicRef xlink:href="#broader"/>      </roleSpec>      <topicRef xlink:href="#https://vocabulario.abcd.usp.br/pt-br/?tema=68073"/>    </member>  </association></topicMap>